Non-carcinoma malignancies of the pancreas are very rare.
Primary lymphoma of the pancreas makes up about 1 in 200 cases of pancreatic tumours. The presentation and clinical appearance may be similar to ductal adenocarcinoma. These cases may be curable in some settings. Most mature B cell neoplasms have been described (eg. diffuse large B cell, follicular and extranodal marginal zone lymphoma).
There are very few case reports of primary pancreatic sarcoma.
A tumour of children, also extremely rare. It usually presents with an abdominal mass. Metastases are frequent but the tumour is curable if detected before they have developed.