b) Desmoid-type Fibromatosis

Treatment of peripheral desmoid tumours

Surgical excision may be curative but to achieve positive margins extensive and deforming surgery may be necessary. Radiotherapy is often used in the adjuvant setting to improve local control. A dose of 50 Gy in 25 fractions is the minimum required, but improves local control significantly.

See Baumert et al (2007) The impact of radiotherapy in the treatment of desmoid tumours. An international survey of 110 patients. A study of the Rare Cancer Network